Assuntos
Pessoa de Meia-Idade , Feminino , Humanos , Carcinoma de Células Escamosas/secundário , Neoplasias Musculares/secundário , Neoplasias Pulmonares/patologia , Carcinoma de Células Escamosas , Evolução Fatal , Espectroscopia de Ressonância Magnética , Neoplasias Musculares , Neoplasias PulmonaresAssuntos
Pessoa de Meia-Idade , Feminino , Humanos , Carcinoma de Células Escamosas/secundário , Neoplasias Pulmonares/patologia , Neoplasias Musculares/secundário , Carcinoma de Células Escamosas/diagnóstico por imagem , Evolução Fatal , Neoplasias Pulmonares/diagnóstico por imagem , Espectroscopia de Ressonância Magnética , Neoplasias Musculares/diagnóstico por imagemAssuntos
Pessoa de Meia-Idade , Feminino , Humanos , Carcinoma de Células Escamosas/secundário , Neoplasias Pulmonares/patologia , Neoplasias Musculares/secundário , Carcinoma de Células Escamosas/diagnóstico por imagem , Evolução Fatal , Neoplasias Pulmonares/diagnóstico por imagem , Espectroscopia de Ressonância Magnética , Neoplasias Musculares/diagnóstico por imagemRESUMO
Catastrophic antiphospholipid syndrome (CAPS) is an acutely devastating situation characterized by widespread thrombotic microangiopathy in the presence of elevated titers of antiphospholipid antibodies. We describe a 57-year old woman who underwent liver transplantation for primary sclerosing cholangitis and developed this malignant variant of the antiphospholipid syndrome.
Assuntos
Síndrome Antifosfolipídica/etiologia , Transplante de Fígado/efeitos adversos , Complicações Pós-Operatórias , Colangite Esclerosante/cirurgia , Feminino , Humanos , Pessoa de Meia-IdadeRESUMO
We describe a 26-year-old white female with a history of Raynaud phenomenon, erythema nodosum, polyarthralgias, migraine, vertigo, seizures, transient ischemic attacks, one fetal loss, and false positive VDRL, who developed milk hypertension without overt lupus nephritis. She had positive antinuclear antibodies (ANA) and double-stranded deoxyribonucleic acid (dsDNA) antibodies. The lupus anticoagulant test (LAC) and cardiolipins antibodies (aCL) were positive. She was diagnosed as having a Systemic Lupus Erythematosus-like illness (SLE-like) with 'secondary' antiphospholipid syndrome (APS). Renal spiral computed tomography (CT) with intravenous (IV) contrast showed bilateral renal artery stenosis. Anticoagulation with acenocumarol was started. She became normotensive without antihypertensive drugs five months later. A follow-up renal spiral CT showed complete recanalization of both renal arteries, making thrombosis the more likely culprit pathology in the stenosis. After two years follow up the patient is normotensive. She remains on acenocumarol.